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Cystic Fibrosis

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Nursing Diagnosis:
Ineffective airway clearance R/T increased pulmonary secretions AEB Patient has thick purulent sputum and crackles noted upon ascultation

Nursing Diagnosis:
Risk for infection R/T tenacious secretions and altered body defenses

Medical Management: IV antibiotic treatment with Ceftazidime, CPT, and observation

Medical Diagnosis: Cystic Fibrosis

Signs & Symptoms: Color pale pink with bluish tinged nail beds.

Patient Hx: Patient Initials: J.R.
10 year old white male. No previous injuries, has a history of CF

Goal:
Client will be able to remove secretions from the airway w/i 10 minutes

Goal:
Client will remain free of infections during my shift

Goal: Client’s nutritional status will improve, and the client will exhibit normal growth within 1 week

Nursing Interventions 1) The child should take deep breath and then exhale rapidly while whispering the word huff (forcing expiration) 2) Perform CPT 2 or 3 x’s a day and as needed. Determine child’s respiratory status before and after CPT. 3) Administer ordered bronchodilators or mucolytics in conjunction with any other treatments 4) Elevate head of bed, or support child in an upright position and stay with child during coughing episodes.

Nursing Interventions 1) Monitor the child for s/s of respiratory infection (fever, chills, increased respirations, dyspnea, purulent secretions) 2) Advise the family to avoid exposing the child to others who are ill. 3) Teach parents the importance of getting all routine childhood immunizations at the ages recommended to help prevent any other illnesses. 4) Promote an annual influenza vaccine also if appropriate

Nursing Interventions 1) Provide a well-balanced diet that is high in calories, protein, and carbohydrates and that includes the child’s favorite

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